PUBLICATION

Blind But Alive - Congenital Loss of atoh7 Disrupts the Visual System of Adult Zebrafish

Authors
Hammer, J., Röppenack, P., Yousuf, S., Machate, A., Fischer, M., Hans, S., Brand, M.
ID
ZDB-PUB-241121-9
Date
2024
Source
Investigative ophthalmology & visual science   65: 4242 (Journal)
Registered Authors
Brand, Michael, Fischer, Marika, Hans, Stefan, Machate, Anja
Keywords
none
MeSH Terms
  • Zebrafish Proteins*/genetics
  • Zebrafish Proteins*/metabolism
  • Basic Helix-Loop-Helix Transcription Factors/genetics
  • Basic Helix-Loop-Helix Transcription Factors/metabolism
  • Retinal Ganglion Cells*/metabolism
  • Retinal Ganglion Cells*/pathology
  • Tomography, Optical Coherence*
  • Zebrafish*
  • Animals
  • Optic Nerve/metabolism
  • Optic Nerve/pathology
  • Superior Colliculi/metabolism
  • Superior Colliculi/physiopathology
  • Blindness*/genetics
  • Blindness*/physiopathology
  • Mutation
  • Phenotype
  • Disease Models, Animal*
  • Retina/metabolism
  • Retina/physiopathology
  • Nystagmus, Optokinetic/physiology
  • Immunohistochemistry
PubMed
39565303 Full text @ Invest. Ophthalmol. Vis. Sci.
Abstract
Vision is the predominant sense in most animal species. Loss of vision can be caused by a multitude of factors resulting in anatomic as well as behavioral changes. In mice and zebrafish, atoh7 mutants are completely blind as they fail to generate retinal ganglion cells (RGCs) during development. In contrast to mice, raising blind zebrafish to adulthood is challenging and this important model is currently missing in the field. Here, we report the phenotype of homozygous mutant adult zebrafish atoh7 mutants that have been raised using adjusted feeding and holding conditions.
The phenotype of adult mutants was characterized using classical histology and immunohistochemistry as well as optical coherence tomography. In addition, the optokinetic response was characterized.
Adult atoh7 mutants display dark body pigmentation and significantly reduced body length. They fail to form RGCs, the resulting nerve fiber layer as well as the optic nerve, and consequently behave completely blindly. In contrast, increased amounts of other retinal neurons and Müller glia are formed. In addition, the optic tectum is anatomically reduced in size, presumably due to the missing retinal input.
Taken together, we provide a comprehensive characterization of a completely blind adult zebrafish mutant with focus on retinal and tectal morphology, as a useful model for glaucoma and optic nerve aplasia.
Genes / Markers
Figures
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Expression
Phenotype
Mutations / Transgenics
Human Disease / Model
Sequence Targeting Reagents
Fish
Antibodies
Orthology
Engineered Foreign Genes
Mapping