spindle cell rhabdomyosarcoma

Term ID

DOID:3260

Synonyms

• Sclerosing rhabdomyosarcoma
• Spindle Cell/Sclerosing Rhabdomyosarcoma
• Synonym Rhabdomyosarcoma, spindle cell/sclerosing type

Definition

A rhabdomyosarcoma that is characterized by the presence of whorls of spindle cells forming a storiform pattern. In children it usually arises in the paratesticular region. In adults it usually arises from the deep soft tissues in the head and neck. https://pubmed.ncbi.nlm.nih.gov/34958505/

References

• ICDO:8912/3
• NCI:C6519
• SNOMEDCT_US_2023_03_01:404055006
• UMLS_CUI:C1266134

Ontology

Human Disease   ( DOID:3260 )