Search Ontology:
ChEBI

nitisinone

Term ID
CHEBI:50378
Synonyms
  • 2-(alpha,alpha,alpha-Trifluoro-2-nitro-p-tuluoyl)-1,3-cyclohexanedione
  • 2-[2-nitro-4-(trifluoromethyl)benzoyl]cyclohexane-1,3-dione
  • nitisinona
  • nitisinone
  • nitisinonum
  • Orfadin
Definition
A cyclohexanone that is cyclohexane-1,3-dione substituted at position 2 by a 2-nitro-4-(trifluoromethyl)benzoyl group. It is used in the treatment of hereditary tyrosinemia type 1.
References
Ontology
ChEBI  ( EBI )
Relationships
is a type of
has_role
Phenotype
Phenotype resulting from nitisinone
Phenotype where environments contain nitisinone
Phenotype modified by environments containing nitisinone
Human Disease / Model Data
Citations