acute interstitial pneumonia

Term ID

DOID:2800

Synonyms

• accelerated interstitial pneumonia
• acute interstitial pneumonitis
• AIP
• Hamman-Rich disease
• Hamman-Rich syndrome
• Idiopathic pulmonary fibrosis, acute fatal form

Definition

A idiopathic interstitial pneumonia which develops suddenly and is severe. Initially, the lung shows edema, hyaline membranes, and interstitial acute inflammation. Later, it develops loose organizing fibrosis, mostly within alveolar septa and type II pneumocyte hyperplasia. Fever, cough, and difficulty breathing develop over 1 to 2 weeks, typically progressing to acute respiratory failure. (2)

References

• GARD:12835
• ICD10CM:J84.114
• ICD9CM:516.33
• NCI:C35806
• ORDO:79126
• SNOMEDCT_US_2023_03_01:129459004
• UMLS_CUI:C1279945

Ontology

Human Disease   ( DOID:2800 )