obsolete Jensen syndrome

Term ID

DOID:0050867

Synonyms

• opticoacoustic nerve atrophy with dementia

Definition

A syndrome that is characterized by sensorineural hearing loss with onset in infancy, followed in adolescence by progressive optic nerve atrophy with loss of vision and in adulthood by progressive dementia. (3)

References

Obsolete

true

Secondary ID:

Merged into

deafness-dystonia-optic neuronopathy syndrome

Ontology

  ( DOID:0050867 )