scimitar syndrome

Term ID

DOID:4297

Synonyms

• congenital venolobar syndrome
• Halasz syndrome
• hypogenetic lung syndrome
• mirror-image lung syndrome
• pulmonary venolobar syndrome
• total anomalous pulmonary venous return
• vena cava bronchovascular syndrome

Definition

A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung. (2)

References

• ICD10CM:Q26.8
• MESH:D012587
• NCI:C85056
• OMIM:106700
• ORDO:185
• SNOMEDCT_US_2023_03_01:39905002
• UMLS_CUI:C0036400

Ontology

Human Disease   ( DOID:4297 )