Search Ontology:
Human Disease

congenital hypomyelinating neuropathy 1

Term ID
DOID:0110195
Synonyms
  • autosomal recessive congenital hypomyelinating or amyelinating neuropathy
  • Charcot-Marie-Tooth disease type 4E
  • Charcot-Marie-Tooth neuropathy type 4E
  • CHN1
  • CMT4E
  • Neuropathy, congenital hypomyelinating, 1
Definition
A congenital hypomyelinating neuropathy that has_material_basis_in homozygous or heterozygous mutation in the EGR2 gene on chromosome 10q21. https://www.ncbi.nlm.nih.gov/pubmed/9537424
References
  • ICD10CM:G60.0
  • MIM:605253
  • ORDO:99951
  • SNOMEDCT_US_2025_09_01:763135001
  • UMLS_CUI:C4721437
Ontology
Human Disease   ( DOID:0110195 )
Relationships
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Genes Involved
Zebrafish Models