Search Ontology:
Human Disease

blastic plasmacytoid dendritic cell neoplasm

Term ID
DOID:0081076
Synonyms
  • Agranular CD4+ CD56+ Hematodermic Neoplasm/Tumor
  • Agranular CD4+ Natural Killer Cell Leukemia
  • Blastic Natural Killer Leukemia/Lymphoma
  • Blastic NK-Cell Lymphoma
  • CD4+/CD56+ Hematodermic Neoplasm
  • natural killer (NK) cell leukemia/lymphoma
Definition
An acute leukemia that is derived from the precursors of plasmacytoid dendritic cells, with a high frequency of cutaneous and bone marrow involvement and leukemic dissemination. Skin lesions appearing on the arms, legs, face and neck are the most common BPDCN symptom. Other symptoms include low counts of healthy blood cells and swollen lymph nodes. (3)
References
  • NCI:C7203
Ontology
Human Disease   ( DOID:0081076 )
Relationships
is a type of
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Genes Involved
Zebrafish Models