subcutaneous panniculitis-like T-cell lymphoma

Term ID

DOID:0070662

Synonyms

• SPTCL

Definition

A primary cutaneous T-cell non-Hodgkin lymphoma characterized by infiltration of subcutaneous tissue by neoplastic alpha-beta cytotoxic T cells mimicking panniculitis. Homozygous or compound heterozygous mutation in the HAVCR2 gene may contribute to development of this disease, with some evidence of incomplete penetrance. (3)

References

• ICD10CM:C86.3
• ICDO:9708/3
• MESH:C537503
• MIM:618398
• NCI:C6918
• ORDO:86884
• SNOMEDCT_US_2025_09_01:404133000
• UMLS_CUI:C0522624

Ontology

Human Disease   ( DOID:0070662 )