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Human Disease

maple syrup urine disease type II

Term ID
DOID:0061207
Synonyms
Definition
A maple syrup urine disease that has_material_basis_in homozygous or compound heterozygous mutation in the DBT gene, which encodes a subunit of the branched-chain alpha-keto acid dehydrogenase complex (BCKDC), on chromosome 1p21. https://pubmed.ncbi.nlm.nih.gov/17922217/
References
Ontology
Human Disease   ( DOID:0061207 )
Relationships
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Genes Involved
Zebrafish Models