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Human Disease

autosomal dominant autoinflammation, panniculitis, and dermatosis syndrome

Term ID
DOID:0061169
Synonyms
Definition
An autoinflammation, panniculitis, and dermatosis syndrome characterized by the onset of autoinflammatory features in infancy, including fever, aseptic skin lesions, panniculitis, and poor wound healing that has_material_basis_in heterozygous dominant-negative mutation in the OTULIN gene on chromosome 5p15. (2)
References
Ontology
Human Disease   ( DOID:0061169 )
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Genes Involved
Zebrafish Models