Search Ontology:
ChEBI
nitisinone
- Term ID
- CHEBI:50378
- Synonyms
-
- 2-(alpha,alpha,alpha-Trifluoro-2-nitro-p-tuluoyl)-1,3-cyclohexanedione
- 2-[2-nitro-4-(trifluoromethyl)benzoyl]cyclohexane-1,3-dione
- nitisinona
- nitisinone
- nitisinonum
- Orfadin
- Definition
- A cyclohexanone that is cyclohexane-1,3-dione substituted at position 2 by a 2-nitro-4-(trifluoromethyl)benzoyl group. It is used in the treatment of hereditary tyrosinemia type 1.
- References
-
- cas:104206-65-7
- drugbank:DB00348
- drugcentral:1944
- hmdb:HMDB0014492
- kegg.drug:D05177
- patent:EP186118
- patent:US4774360
- patent:US5006158
- patent:US5550165
- patent:US5668089
- pubmed:14668946
- pubmed:15297036
- pubmed:17152330
- pubmed:17458044
- pubmed:20883679
- pubmed:21377430
- pubmed:21620748
- pubmed:21752152
- pubmed:21813063
- pubmed:21968107
- pubmed:21968110
- pubmed:22456946
- pubmed:22885033
- pubmed:23146787
- pubmed:23203167
- pubmed:23250512
- pubmed:23311542
- pubmed:23430914
- pubmed:23430917
- pubmed:23486607
- pubmed:23511227
- reaxys:8639943
- wikipedia.en:Nitisinone
- Ontology
- ChEBI ( EBI )
Phenotype
Phenotype resulting from nitisinone
Phenotype where environments contain nitisinone
Phenotype modified by environments containing nitisinone
Phenotype affecting nitisinone
Human Disease Model