Search Ontology:
ChEBI
4-methyl-2-oxopentanoic acid
- Term ID
- CHEBI:48430
- Synonyms
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- 2-OXO-4-METHYLPENTANOIC ACID
- 2-Oxoisocaproate
- 4-Methyl-2-oxopentanoate
- 4-methyl-2-oxopentanoic acid
- 4-methyl-2-oxovaleric acid
- alpha-ketoisocaproic acid
- Ketoleucine
- Definition
- A 2-oxo monocarboxylic acid that is pentanoic acid (valeric acid) substituted with a keto group at C-2 and a methyl group at C-4. A metabolite that has been found to accumulate in maple syrup urine disease.
- References
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- CAS:816-66-0
- DrugBank:DB03229
- HMDB:HMDB0000695
- KEGG:C00233
- KNApSAcK:C00019677
- MetaCyc:2K-4CH3-PENTANOATE
- PDBeChem:COI
- PMID:14636955
- PMID:22770225
- Reaxys:1701823
- Ontology
- ChEBI ( EBI )
- Resources
- CTD
- is a type of
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- has_functional_parent
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- has_role
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- inverse is_conjugate_base_of
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- is_conjugate_acid_of
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Show first 5 Terms
Phenotype
Phenotype resulting from 4-methyl-2-oxopentanoic acid
Phenotype where environments contain 4-methyl-2-oxopentanoic acid
Phenotype modified by environments containing 4-methyl-2-oxopentanoic acid
Human Disease Model