Search Ontology:
ChEBI
3-methyl-2-oxovaleric acid
- Term ID
- CHEBI:35932
- Synonyms
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- 2-Oxo-3-methyl-n-valeric acid
- 2-Oxo-3-methylpentanoic acid
- 2-Oxo-3-methylvalerate
- 2-Oxo-3-methylvaleric acid
- 2-Oxoisoleucine
- 2-oxokolavenic acid
- 3-ethyl-3-methylpyruvic acid
- 3-methyl-2-oxopentanoic acid
- 3-methyl-2-oxovaleric acid
- alpha-keto-beta-methyl-n-valeric acid
- alpha-keto-beta-methylvaleric acid
- alpha-oxo-beta-methyl-n-valeric acid
- alpha-Oxo-beta-methylvaleric acid
- ketoisoleucine
- Definition
- A 2-oxo monocarboxylic acid that is valeric acid carrying oxo- and methyl substituents at C-2 and C-3, respectively. An alpha-keto acid analogue and metabolite of isoleucine in man, animals and bacteria. Used as a clinical marker for maple syrup urine disease (MSUD).
- References
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- CAS:1460-34-0
- Gmelin:971983
- HMDB:HMDB0000491
- KEGG:C03465
- PMID:1638756
- PMID:17190852
- PMID:759179
- Reaxys:1098987
- Ontology
- ChEBI ( EBI )
- Resources
- CTD
- is a type of
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- has subtype
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- has_functional_parent
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- has_role
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- inverse is_conjugate_base_of
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- is_conjugate_acid_of
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Phenotype
Phenotype resulting from 3-methyl-2-oxovaleric acid
Phenotype where environments contain 3-methyl-2-oxovaleric acid
Phenotype modified by environments containing 3-methyl-2-oxovaleric acid
Human Disease Model