Search Ontology:
ChEBI

3-methyl-2-oxovaleric acid

Term ID
CHEBI:35932
Synonyms
  • 2-Oxo-3-methyl-n-valeric acid
  • 2-Oxo-3-methylpentanoic acid
  • 2-Oxo-3-methylvalerate
  • 2-Oxo-3-methylvaleric acid
  • 2-Oxoisoleucine
  • 2-oxokolavenic acid
  • 3-ethyl-3-methylpyruvic acid
  • 3-methyl-2-oxopentanoic acid
  • 3-methyl-2-oxovaleric acid
  • alpha-keto-beta-methyl-n-valeric acid
  • alpha-keto-beta-methylvaleric acid
  • alpha-oxo-beta-methyl-n-valeric acid
  • alpha-Oxo-beta-methylvaleric acid
  • ketoisoleucine
Definition
A 2-oxo monocarboxylic acid that is valeric acid carrying oxo- and methyl substituents at C-2 and C-3, respectively. An alpha-keto acid analogue and metabolite of isoleucine in man, animals and bacteria. Used as a clinical marker for maple syrup urine disease (MSUD).
References
Ontology
ChEBI  ( EBI )
Resources
CTD
Relationships
is a type of
has subtype
has_functional_parent
has_role
inverse is_conjugate_base_of
is_conjugate_acid_of
Phenotype
Phenotype resulting from 3-methyl-2-oxovaleric acid
Phenotype where environments contain 3-methyl-2-oxovaleric acid
Phenotype modified by environments containing 3-methyl-2-oxovaleric acid
Human Disease Model