Search Ontology:
ChEBI

sapropterin dihydrochloride

Term ID
CHEBI:32120
Synonyms
  • (6R)-2-amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydropteridin-4(3H)-one dihydrochloride
  • (6R)-tetrahydrobiopterin dihydrochloride
  • (6R)-tetrahydrobiopterin hydrochloride
  • sapropterin 2HCl
  • sapropterin dihydrochloride
  • sapropterin hydrochloride
Definition
The dihydrochloride salt of sapropterin. It is used for the diagnosis and treatment of variant forms of phenylketonuria (hyperphenylalaninaemia) associated with tetrahydrobiopterin deficiency. Natural cofactor for phenylalanine hydroxylase, tyrosine hydroxylase, tryptophan hydroxylase, and nitric oxide synthetase.
References
Ontology
ChEBI  ( EBI )
Relationships
is a type of
has_part
has_role
Phenotype
Phenotype resulting from sapropterin dihydrochloride
Phenotype where environments contain sapropterin dihydrochloride
Phenotype modified by environments containing sapropterin dihydrochloride
Human Disease Model
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