OBO ID: CHEBI:50378
Term Name: nitisinone Search Ontology:
Synonyms:
  • 2-(alpha,alpha,alpha-Trifluoro-2-nitro-p-tuluoyl)-1,3-cyclohexanedione
  • 2-[2-nitro-4-(trifluoromethyl)benzoyl]cyclohexane-1,3-dione
  • nitisinona
  • nitisinone
  • nitisinonum
  • Orfadin
Definition: A cyclohexanone that is cyclohexane-1,3-dione substituted at position 2 by a 2-nitro-4-(trifluoromethyl)benzoyl group. It is used in the treatment of hereditary tyrosinemia type 1.
References:
Ontology: ChEBI  ( EBI )
PHENOTYPE No data available