PUBLICATION

Establishing a Zebrafish Functional Assay to Assess the Pathogenicity of Variants of Uncertain Significance in Ciliopathies

Authors
Aresi, C., Tonelli, F., Mazzotta, C., Serpieri, V., Masiero, C., Torriani, C., Villani, S., Valente, E.M., Forlino, A.
ID
ZDB-PUB-260512-1
Date
2026
Source
European journal of clinical investigation   56: e70220e70220 (Journal)
Registered Authors
Forlino, Antonella, Tonelli, Francesca
Keywords
VUSs, ciliopathies, morpholino, zebrafish
MeSH Terms
none
PubMed
42116549 Full text @ Eur J Clin Invest
Abstract
A zebrafish morpholino knockdown model targeting ahi1 enables efficient phenotypic assessment of ciliopathy-related defects and functional evaluation of variants of uncertain significance. This assay clarifies the impact of VUSs, supporting zebrafish morphants as a reliable platform for validating ciliopathy-associated genetic variants.
Genes / Markers
Figures
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Expression
Phenotype
Mutations / Transgenics
Human Disease / Model
Sequence Targeting Reagents
Fish
Antibodies
Orthology
Engineered Foreign Genes
Mapping