PUBLICATION

Ppid is Necessary for Overnutrition-Induced β-cell Loss

Authors
Covington, B.A., Tang, Z., Maddison, L.A., Yang, B., Chen, W.
ID
ZDB-PUB-251216-2
Date
2025
Source
American journal of physiology. Endocrinology and metabolism   330: E152-E160 (Journal)
Registered Authors
Chen, Wenbiao
Keywords
PPID, Zebrafish, beta cell death, diabetes, inflammation
MeSH Terms
  • Animals
  • Animals, Genetically Modified
  • Cell Death/drug effects
  • Cell Death/genetics
  • Cyclophilins*/antagonists & inhibitors
  • Cyclophilins*/genetics
  • Cyclophilins*/metabolism
  • Cyclosporine/pharmacology
  • Insulin Resistance
  • Insulin-Secreting Cells*/drug effects
  • Insulin-Secreting Cells*/metabolism
  • Insulin-Secreting Cells*/pathology
  • Mitochondria/metabolism
  • Mitochondrial Membrane Transport Proteins/metabolism
  • Mitochondrial Permeability Transition Pore
  • Overnutrition*/complications
  • Overnutrition*/metabolism
  • Overnutrition*/pathology
  • Peptidyl-Prolyl Isomerase F*/genetics
  • Peptidyl-Prolyl Isomerase F*/metabolism
  • Reactive Oxygen Species/metabolism
  • Zebrafish
  • Zebrafish Proteins*/genetics
  • Zebrafish Proteins*/metabolism
PubMed
41397247 Full text @ Am. J. Physiol. Endocrinol. Metab.
Abstract
Type 2 diabetes (T2D) involves progressive loss of functional β-cell mass. In a zebrafish insulin-resistant model (zMIR), overnutrition triggers islet inflammation and nocturnal β-cell death. The cell death is prevented by the cyclophilin D (Ppid) inhibitor, cyclosporin A (CsA). Reducing mitochondrial ROS with mito-TEMPO or mitochondrial calcium with Ru360 protects β cells, further implicating the mitochondrial permeability transition pore (mPTP) in β-cell loss. The timing of β-cell death coincides with lower mitochondrial antioxidant gene expression, indicating diurnal mitochondrial vulnerability. Global ppid-/- preserves β-cell mass without altering islet inflammation or macrophage recruitment. Conversely, β-cell-specific PPID re-expression restores-and exacerbates-β-cell loss, which remains CsA-sensitive. These findings identify Ppid as a β-cell-intrinsic mediator of overnutrition-induced β-cell loss.
Genes / Markers
Figures
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Expression
Phenotype
Mutations / Transgenics
Human Disease / Model
Sequence Targeting Reagents
Fish
Antibodies
Orthology
Engineered Foreign Genes
Mapping