PUBLICATION

Martinostat as a novel HDAC inhibitor to overcome tyrosine kinase inhibitor resistance in chronic myeloid leukemia

Authors
Yang, H., Li, V., Park, S.J., Cheon, S.W., Lorant, A., Mazumder, A., Lee, J.Y., Orlikova-Boyer, B., Cerella, C., Christov, C., Kirsch, G., Olberg, D.E., Bormans, G., Kang, H.J., Han, B.W., Schnekenburger, M., Diederich, M.
ID
ZDB-PUB-250717-11
Date
2025
Source
Clinical epigenetics   17: 125 (Journal)
Registered Authors
Keywords
Cell death, Chronic myeloid leukemia, Combination treatment, HDAC inhibitors, Imatinib resistance
MeSH Terms
  • Animals
  • Apoptosis/drug effects
  • Cell Line, Tumor
  • Cell Proliferation/drug effects
  • Drug Resistance, Neoplasm*/drug effects
  • Histone Deacetylase Inhibitors*/pharmacology
  • Histone Deacetylase Inhibitors*/therapeutic use
  • Humans
  • Imatinib Mesylate/pharmacology
  • Imatinib Mesylate/therapeutic use
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive*/drug therapy
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive*/genetics
  • Mice
  • Protein Kinase Inhibitors*/pharmacology
  • Protein Kinase Inhibitors*/therapeutic use
  • Tyrosine Kinase Inhibitors
  • Xenograft Model Antitumor Assays
  • Zebrafish
PubMed
40671124 Full text @ Clin Epigenetics
Abstract
Chronic myeloid leukemia (CML) remains a therapeutic challenge, particularly in patients who develop resistance to standard tyrosine kinase inhibitors (TKIs) such as imatinib. Here, we present the first demonstration of the potent anti-leukemic activity of the histone deacetylase (HDAC) inhibitor martinostat in both TKI-sensitive and TKI-resistant CML.
Structural and biochemical analyses confirmed the efficient and selective binding of martinostat to HDAC isoenzyme ligand-binding pockets, resulting in histone and tubulin hyperacetylation in both imatinib-sensitive and resistant CML cells, outperforming vorinostat, a clinically used HDAC inhibitor (HDACi). It selectively impaired CML cell proliferation and viability and induced apoptosis across various CML models, including resistant cell models and patient blasts, with minimal toxicity to healthy cells and low developmental toxicity in zebrafish. In addition to its single-agent efficacy, martinostat demonstrated enhanced anticancer effects when combined with imatinib, both in vitro and in vivo, significantly reducing tumor growth in resistant CML xenograft models. Mechanistically, mRNA-seq data showed that martinostat disrupted key survival signaling pathways and amplified apoptotic responses, contributing to its anticancer activity.
These findings highlight the potential of martinostat as a selective, low-toxicity HDACi that, combined with TKIs, could provide an effective strategy to overcome drug resistance in CML and improve therapeutic outcomes.
Genes / Markers
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Human Disease / Model
Sequence Targeting Reagents
Fish
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Orthology
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Mapping