PUBLICATION

BETA-AMYLOID DEPOSIT IN BILIARY ATRESIA REDUCES LIVER REGENERATION VIA INHIBITING ENERGY METABOLISM AND mTOR SIGNALING

Authors
Tian, X., Wang, Y., Zhou, Y., Wu, B., Lu, Y., Du, J., Wang, W., Cai, W., Xiao, Y.
ID
ZDB-PUB-220923-17
Date
2022
Source
Clinical and translational gastroenterology   13(11): e00536 (Journal)
Registered Authors
Keywords
none
MeSH Terms
  • Humans
  • Animals
  • Mice
  • Energy Metabolism
  • TOR Serine-Threonine Kinases
  • Liver Regeneration*
  • Biliary Atresia*
  • Zebrafish
PubMed
36137184 Full text @ Clin Transl Gastroenterol
Abstract
Biliary atresia (BA) is a devastating obstructive bile duct disease of newborns. This study aims to investigate the roles and involved mechanisms of beta-amyloid (Aβ) in the pathogenesis of BA.
We examined the distribution of Aβ protein and its precursor in the livers of BA patients. A murine liver organoid and a zebrafish model were established to investigate the exact roles of Aβ in liver regeneration for BA.
Both Aβ mRNA and protein significantly increased in livers of BA infants and deposited around the central vein. In the plasma, Aβ elevated significantly in BA patients and positively correlated with liver injury progression. In vitro, Aβ treatment induced abnormal morphology and caused impaired growth in liver organoids. Energy metabolism analysis demonstrated Aβ increased aerobic glycolysis and reduced ATP synthase in organoids, in which the mammalian target of rapamycin (mTOR) signaling was suppressed. In vivo, Aβ42 exposure caused liver degeneration in zebrafish larvae.
Aβ depositing in livers of BA infants reduced the liver regeneration via attenuating mitochondrial respiration and mTOR signaling.
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