PUBLICATION

The non-canonical NF-κB pathway promotes NPC2 expression and regulates intracellular cholesterol trafficking

Authors
Liao, Y., Wei, J., Wang, J., Shi, X., Luo, J., Song, B.L.
ID
ZDB-PUB-180810-8
Date
2018
Source
Science China. Life sciences   61(10): 1222-1232 (Journal)
Registered Authors
Keywords
NF-κB2, NPC2, cholesterol transport, transcriptional regulation
MeSH Terms
  • Animals
  • Biological Transport
  • Carrier Proteins/genetics
  • Carrier Proteins/metabolism*
  • Cell Line
  • Cell Line, Tumor
  • Cells, Cultured
  • Cholesterol/metabolism*
  • Embryo, Nonmammalian/metabolism
  • Glycoproteins/genetics
  • Glycoproteins/metabolism*
  • HeLa Cells
  • Humans
  • Intracellular Space/metabolism
  • Mice, Knockout
  • Microscopy, Confocal
  • NF-kappa B p52 Subunit/genetics
  • NF-kappa B p52 Subunit/metabolism*
  • RNA Interference
  • Signal Transduction*
  • Zebrafish
PubMed
30091016 Full text @ Sci. China Ser. C-Life Sci.
Abstract
Niemann-Pick type C2 (NPC2) is a lysosome luminal protein that functions in concert with NPC1 to mediate egress of low-density lipoprotein-derived cholesterol from lysosome. The nuclear factor kappa B subunit 2 (NF-κB2) protein is a component of NF-κB transcription factor complex critically implicated in immune and inflammatory responses. Here, we report that NF-κB2 regulates intracellular cholesterol transport by controlling NPC2 expression. RNAi-mediated disruption of NF-κB2, as well as other signaling members of the non-canonical NF-κB pathway, caused intracellular cholesterol accumulation. Blockage of the non-canonical NF-κB pathway suppressed NPC2 expression, whereas Lymphotoxin β receptor (LTβR) activation or Baff receptor (BaffR) stimulation up-regulated the mRNA abundance and protein level of NPC2. Further, NF-κB2 activated NPC2 transcription through direct binding to its promoter region. We also observed cholesterol accumulation in NF-κB2-deficient zebrafish embryo and NF-κB2 mutant mice. Collectively, these data identify a regulatory role for the non-canonical NF-κB pathway in intracellular cholesterol trafficking and suggest a link between cholesterol transport and immune system.
Genes / Markers
Figures
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Expression
Phenotype
Mutations / Transgenics
Human Disease / Model
Sequence Targeting Reagents
Fish
Antibodies
Orthology
Engineered Foreign Genes
Mapping