Search Ontology:
ChEBI
2-hydroxy-4-methylvaleric acid
- Term ID
- CHEBI:59783
- Synonyms
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- 2-hydroxy-4-methylpentanoic acid
- 2-hydroxyisocaproic acid
- 2-hydroxyisohexanoic acid
- alpha-Hydroxyisocaproic acid
- Leucic acid
- leucinic acid
- Definition
- A valeric acid derivative having a hydroxy substituent at the 2-position and a methyl substituent at the 4-position; an alpha-hydroxy analogue of leucine. A bacterial metabolite, it has also been isolated from amniotic fluid, was found in a patient with dihydrolipoyl dehydrogenase deficiency and is present in the urine of patients with short bowel syndrome.
- References
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- CAS:498-36-2
- HMDB:HMDB0000665
- LIPID_MAPS_instance:LMFA01050381
- PMID:17439666
- PMID:4018104
- PMID:6467607
- PMID:6688766
- Reaxys:1721733
- Ontology
- ChEBI ( EBI )
- Resources
- CTD
- is a type of
-
- has subtype
-
- has_functional_parent
-
- has_role
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- inverse is_conjugate_base_of
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- is_conjugate_acid_of
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Phenotype
Phenotype resulting from 2-hydroxy-4-methylvaleric acid
Phenotype where environments contain 2-hydroxy-4-methylvaleric acid
Phenotype modified by environments containing 2-hydroxy-4-methylvaleric acid
Human Disease Model