Search Ontology:
ChEBI

beta-D-GalNAc-(1->4)-[alpha-Neu5Ac-(2->3)]-beta-D-Gal-(1->4)-beta-D-Glc-(1<->1')-Cer

Term ID
CHEBI:51013
Synonyms
  • (2S,3R,4E)-2-alkanamido-3-hydroxyoctadec-4-en-1-yl 2-acetamido-2-deoxy-beta-D-galactopyranosyl-(1->4)-[5-acetamido-3,5-dideoxy-D-glycero-alpha-D-galacto-non-2-ulopyranonosyl-(2->3)]-beta-D-galactopyranosyl-(1->4)-beta-D-glucopyranoside
  • (Gal)1 (GalNAc)1 (Glc)1 (Neu5Ac)1 (Cer)1
  • beta-D-GalNAc-(1->4)-[alpha-Neu5Ac-(2->3)]-beta-D-Gal-(1->4)-beta-D-Glc-(1<->1')-Cer
  • ganglioside GM2
  • GM2
  • monosialoganglioside GM2
  • N-Acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
  • N-Acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosylceramide
  • Tay-Sachs ganglioside
Definition
A sialotriaosylceramide consisting of the tetrasaccharide β-D-GalNAc-(1→4)-[α-Neu5Ac-(2→3)]-β-D-Gal-(1→4)-β-D-Glc attached to the primary hydroxy function of ceramide.
References
  • kegg.compound:C04884
  • kegg.glycan:G00109
  • patent:WO0123431
  • pubmed:1371229
  • pubmed:15546874
  • pubmed:18207611
  • pubmed:19130519
  • pubmed:2457654
  • pubmed:2564593
  • pubmed:25867522
  • pubmed:26050638
  • pubmed:28416698
  • pubmed:2933632
  • pubmed:333030
  • pubmed:6210531
  • pubmed:6214725
  • pubmed:6225718
  • pubmed:7243492
  • pubmed:8250149
Ontology
ChEBI  ( EBI )
Relationships
Phenotype
Phenotype resulting from beta-D-GalNAc-(1->4)-[alpha-Neu5Ac-(2->3)]-beta-D-Gal-(1->4)-beta-D-Glc-(1<->1')-Cer
Phenotype where environments contain beta-D-GalNAc-(1->4)-[alpha-Neu5Ac-(2->3)]-beta-D-Gal-(1->4)-beta-D-Glc-(1<->1')-Cer
Phenotype modified by environments containing beta-D-GalNAc-(1->4)-[alpha-Neu5Ac-(2->3)]-beta-D-Gal-(1->4)-beta-D-Glc-(1<->1')-Cer
Phenotype affecting beta-D-GalNAc-(1->4)-[alpha-Neu5Ac-(2->3)]-beta-D-Gal-(1->4)-beta-D-Glc-(1<->1')-Cer
Human Disease Model