Mahmood et al., 2013 - A zebrafish model of CLN2 disease is deficient in tripeptidyl peptidase 1 and displays progressive neurodegeneration accompanied by a reduction in proliferation. Brain : a journal of neurology   136(Pt 5):1488-507 Full text @ Brain
Human Disease / Model Data (1 Record)
Human Disease Fish Environment Evidence Code
neuronal ceroid lipofuscinosis 2 tpp1sa11/sa11 standard conditions