OBO ID: CHEBI:59783
Term Name: 2-hydroxy-4-methylvaleric acid Search Ontology:
Synonyms:
  • 2-hydroxy-4-methylpentanoic acid
  • 2-hydroxyisocaproic acid
  • 2-hydroxyisohexanoic acid
  • alpha-Hydroxyisocaproic acid
  • Leucic acid
  • leucinic acid
Definition: A valeric acid derivative having a hydroxy substituent at the 2-position and a methyl substituent at the 4-position; an alpha-hydroxy analogue of leucine. A bacterial metabolite, it has also been isolated from amniotic fluid, was found in a patient with dihydrolipoyl dehydrogenase deficiency and is present in the urine of patients with short bowel syndrome.
References:
Ontology: Chebi
PHENOTYPE No data available