OBO ID: CHEBI:55534
Term Name: (R)-2-hydroxy-4-methylpentanoic acid Search Ontology:
Synonyms:
  • (2R)-2-hydroxy-4-methylpentanoic acid
  • (R)-2-hydroxy-4-methylpentanoic acid
  • (R)-2-hydroxy-4-methylvaleric acid
  • (R)-2-hydroxyisocaproic acid
  • (R)-leucic acid
  • 2-hydroxy-4-methyl-D-valeric acid
  • alpha-Hydroxyisocaproic acid
  • D-2-hydroxy-4-methylpentanoic acid
  • D-2-hydroxy-4-methylvaleric acid
  • D-2-hydroxyisocaproic acid
  • D-leucic acid
  • delta-leucic acid
  • leucic acid
Definition: The (R)-enantiomer of 2-hydroxy-4-methylpentanoic acid. Found in patients with short-bowel syndrome (an inborn error of metabolism), and in maple syrup urine disease, MSUD.
References:
Ontology: ChEBI  ( EBI )
PHENOTYPE No data available