OBO ID: CHEBI:35932
Term Name: 3-methyl-2-oxovaleric acid Search Ontology:
Synonyms:
  • 2-Oxo-3-methyl-n-valeric acid
  • 2-Oxo-3-methylpentanoic acid
  • 2-Oxo-3-methylvalerate
  • 2-Oxo-3-methylvaleric acid
  • 2-Oxoisoleucine
  • 2-oxokolavenic acid
  • 3-ethyl-3-methylpyruvic acid
  • 3-methyl-2-oxopentanoic acid
  • 3-methyl-2-oxovaleric acid
  • alpha-keto-beta-methyl-n-valeric acid
  • alpha-keto-beta-methylvaleric acid
  • alpha-oxo-beta-methyl-n-valeric acid
  • alpha-Oxo-beta-methylvaleric acid
  • ketoisoleucine
Definition: A 2-oxo monocarboxylic acid that is valeric acid carrying oxo- and methyl substituents at C-2 and C-3, respectively. An alpha-keto acid analogue and metabolite of isoleucine in man, animals and bacteria. Used as a clinical marker for maple syrup urine disease (MSUD).
References:
Ontology: ChEBI  ( EBI )
PHENOTYPE No data available