OBO ID: CHEBI:16831
Term Name: 3-hydroxy-3-methylglutaric acid Search Ontology:
Synonyms:
  • (S)-3-Hydroxy-3-methylglutaric acid
  • (S)-Meglutol
  • 3-HYDROXY-3-METHYL-GLUTARIC ACID
  • 3-Hydroxy-3-methylpentanedioic acid
  • beta-hydroxy-beta-methylglutaric acid
  • Dicrotalic acid
  • meglutol
  • meglutolum
Definition: A dicarboxylic acid that is glutaric acid in which one of the two hydrogens at position 3 is substituted by a hydroxy group, while the other is substituted by a methyl group. It has been found to accumulate in urine of patients suffering from HMG-CoA lyase (3-hydroxy-3-methylglutaryl-CoA lyase, EC 4.1.3.4) deficiency. It occurs as a plant metabolite in Crotalaria dura.
References:
Ontology: ChEBI  ( EBI )
PHENOTYPE No data available