Term Name:	Denys-Drash syndrome
Synonyms:
Definition:	A syndrome that is characterized by the association of diffuse mesangial sclerosis (DMS), male pseudohermaphroditism with a 46,XY karyotype, and nephroblastoma that derives_from an abnormality in the WT1 gene (Wilms' tumor suppressor gene).
Ontology:	Human Disease [DOID:3764]   ( DOID:3764 )