Term Name: | Erdheim-Chester disease |
---|---|
Synonyms: | |
Definition: | A non-Langerhans-cell histiocytosis that is characterized by the proliferation in the tissues of lipid-laden macrophages and the presence of multinucleated giant cells. It results in sclerosis of the long bones and failure of the affected organs. |
Ontology: | Human Disease [DOID:4329] ( DOID:4329 ) |