Term Name: | desmoplastic infantile ganglioglioma / desmoplastic infantile astrocytoma |
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Synonyms: | Desmoplastic Infantile Astrocytoma, desmoplastic infantile ganglioglioma, desmoplastic infantile ganglioglioma and desmoplastic infantile astrocytoma |
Definition: | A ganglioglioma occurring predominantly in the cerebral hemispheres of infants, that are driven by MAPK pathway activation and composed of a mixed astrocytic and neuronal component (DIG) or an astrocytic component only (DIA) embedded in an extensive desmoplastic stroma, often containing foci of undifferentiated embryonal-like tumour cells. |
Ontology: | Human Disease [DOID:0081259] ( DOID:0081259 ) |