| Term Name: | subcutaneous panniculitis-like T-cell lymphoma |
|---|---|
| Synonyms: | SPTCL |
| Definition: | A primary cutaneous T-cell non-Hodgkin lymphoma characterized by infiltration of subcutaneous tissue by neoplastic alpha-beta cytotoxic T cells mimicking panniculitis. Homozygous or compound heterozygous mutation in the HAVCR2 gene may contribute to development of this disease, with some evidence of incomplete penetrance. |
| Ontology: | Human Disease [DOID:0070662] ( DOID:0070662 ) |