| Term Name: | desquamative interstitial pneumonia |
|---|---|
| Synonyms: | familial desquamative interstitial pneumonitis, RBILD, respiratory bronchiolitis-associated interstitial lung disease |
| Definition: | An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation. |
| Ontology: | Human Disease [DOID:0050158] ( DOID:0050158 ) |