Term Name: 4-methyl-2-oxopentanoic acid
Synonyms: 2-OXO-4-METHYLPENTANOIC ACID, 2-Oxoisocaproate, 4-Methyl-2-oxopentanoate, 4-methyl-2-oxopentanoic acid, 4-methyl-2-oxovaleric acid, alpha-ketoisocaproic acid, Ketoleucine
Definition: A 2-oxo monocarboxylic acid that is pentanoic acid (valeric acid) substituted with a keto group at C-2 and a methyl group at C-4. A metabolite that has been found to accumulate in maple syrup urine disease.
Ontology: ChEBI [CHEBI:48430]  ( EBI )

Relationships
is a type of: 2-oxo monocarboxylic acid branched-chain keto acid
has_functional_parent: valeric acid
has_role: algal metabolite human metabolite
inverse is_conjugate_base_of: 4-methyl-2-oxopentanoate
is_conjugate_acid_of: 4-methyl-2-oxopentanoate