UniProt ID: Q5RH02 |
FUNCTION: Copper metallochaperone essential for the synthesis and maturation of cytochrome c oxidase subunit II (MT-CO2/COX2). Involved in transporting copper to the Cu(A) site on MT-CO2/COX2. Also acts as a thiol-disulfide oxidoreductase to regulate the redox state of the cysteines in SCO1 during maturation of MT-CO2/COX2. {ECO:0000250|UniProtKB:O43819}. SUBUNIT: Homodimer. {ECO:0000250|UniProtKB:O43819}. SUBCELLULAR LOCATION: Mitochondrion inner membrane {ECO:0000250|UniProtKB:O43819}; Single-pass membrane protein {ECO:0000255}. SIMILARITY: Belongs to the SCO1/2 family. {ECO:0000305}. |
This information was provided by UniProt through a collaboration with ZFIN. (1) |