OBO ID: DOID:12132
Term Name: granulomatosis with polyangiitis Search Ontology:
Synonyms:
  • Necrotizing respiratory granulomatosis
  • Wegener granulomatosis, formerly
Definition: An autoimmune disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels. https://en.wikipedia.org/wiki/Granulomatosis_with_polyangiitis
References:
  • GARD:7880
  • ICD10CM:M31.3
  • ICD9CM:446.4
  • MESH:D014890
  • NCI:C3444
  • OMIM:608710
  • SNOMEDCT_US_2023_03_01:195353004
  • UMLS_CUI:C3495801
Ontology: Human Disease   ( DOID:12132 )
Relationships
is a type of:
OTHER granulomatosis with polyangiitis PAGES
GENES INVOLVED No data available
ZEBRAFISH MODELS No data available
PHENOTYPE No data available

CITATIONS: None
Your Input Welcome
We welcome your input and comments. Please use this form to recommend updates to the information in ZFIN. We appreciate as much detail as possible and references as appropriate. We will review your comments promptly.
Please check the highlighted fields and try again.
Thank you for submitting comments. Your input has been emailed to ZFIN curators who may contact you if additional information is required.
Oops. Something went wrong. Please try again later.