OBO ID: CHEBI:48430
Term Name: 4-methyl-2-oxopentanoic acid Search Ontology:
Synonyms:
  • 2-OXO-4-METHYLPENTANOIC ACID
  • 2-Oxoisocaproate
  • 4-Methyl-2-oxopentanoate
  • 4-methyl-2-oxopentanoic acid
  • 4-methyl-2-oxovaleric acid
  • alpha-ketoisocaproic acid
  • Ketoleucine
Definition: A 2-oxo monocarboxylic acid that is pentanoic acid (valeric acid) substituted with a keto group at C-2 and a methyl group at C-4. A metabolite that has been found to accumulate in maple syrup urine disease.
References:
  • CAS:816-66-0
  • DrugBank:DB03229
  • HMDB:HMDB0000695
  • KEGG:C00233
  • KNApSAcK:C00019677
  • MetaCyc:2K-4CH3-PENTANOATE
  • PDBeChem:COI
  • PMID:14636955
  • PMID:22770225
  • Reaxys:1701823
Ontology: Chebi
PHENOTYPE No data available