Term Name: | 4-methyl-2-oxopentanoic acid |
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Synonyms: | 2-OXO-4-METHYLPENTANOIC ACID, 2-Oxoisocaproate, 4-Methyl-2-oxopentanoate, 4-methyl-2-oxopentanoic acid, 4-methyl-2-oxovaleric acid, alpha-ketoisocaproic acid, Ketoleucine |
Definition: | A 2-oxo monocarboxylic acid that is pentanoic acid (valeric acid) substituted with a keto group at C-2 and a methyl group at C-4. A metabolite that has been found to accumulate in maple syrup urine disease. |
Ontology: | ChEBI [CHEBI:48430] ( EBI ) |