Term Name: sapropterin
Synonyms: (-)-(6R)-2-amino-6-((1R,2S)-1,2-dihydroxypropyl)-5,6,7,8-tetrahydro-4(3H)-pteridinone, (6R)-2-amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydropteridin-4(3H)-one, (6R)-L-erythro-5,6,7,8-tetrahydrobiopterin, (6R)-L-erythro-tetrahydrobiopterin, 2-Amino-6-(1,2-dihydroxypropyl)-5,6,7,8-tetrahydoro-4(1H)-pteridinone, 5,6,7,8-Tetrahydrobiopterin, 6R-5,6,7,8-tetrahydrobiopterin, 6R-BH4, 6R-L-5,6,7,8-tetrahydrobiopterin, L-erythro-tetrahydrobiopterin, R-THBP, sapropterin, sapropterina, sapropterinum, tetrahydrobiopterin
Definition: A tetrahydropterin that is 2-amino-5,6,7,8-tetrahydropteridin-4(3H)-one in which a hydrogen at position 6 is substituted by a 1,2-dihydroxypropyl group (6R,1'R,2'S-enantiomer).
Ontology: ChEBI [CHEBI:59560]  ( EBI )

Relationships
is a type of: 5,6,7,8-tetrahydrobiopterin
has_role: coenzyme cofactor diagnostic agent human metabolite
inverse has_part: sapropterin dihydrochloride