UniProt ID: A0A2R8RLB4 |
SUBCELLULAR LOCATION: Membrane {ECO:0000256|ARBA:ARBA00004141}; Multi- pass membrane protein {ECO:0000256|ARBA:ARBA00004141}. SIMILARITY: Belongs to the mitochondrial carrier (TC 2.A.29) family. {ECO:0000256|ARBA:ARBA00006375, ECO:0000256|RuleBase:RU000488}. |
UniProt ID: Q0P483 |
FUNCTION: Mitochondrial carrier mediating the transport of coenzyme A (CoA) in mitochondria in exchange for intramitochondrial (deoxy)adenine nucleotides and adenosine 3',5'-diphosphate. {ECO:0000250|UniProtKB:Q86VD7}. CATALYTIC ACTIVITY: Reaction=ADP(out) + CoA(in) = ADP(in) + CoA(out); Xref=Rhea:RHEA:72839, ChEBI:CHEBI:57287, ChEBI:CHEBI:456216; Evidence={ECO:0000250|UniProtKB:Q86VD7}; CATALYTIC ACTIVITY: Reaction=3'-dephospho-CoA(in) + ADP(out) = 3'-dephospho-CoA(out) + ADP(in); Xref=Rhea:RHEA:72843, ChEBI:CHEBI:57328, ChEBI:CHEBI:456216; Evidence={ECO:0000250|UniProtKB:Q86VD7}; CATALYTIC ACTIVITY: Reaction=adenosine 3',5'-bisphosphate(in) + ADP(out) = adenosine 3',5'- bisphosphate(out) + ADP(in); Xref=Rhea:RHEA:72847, ChEBI:CHEBI:58343, ChEBI:CHEBI:456216; Evidence={ECO:0000250|UniProtKB:Q86VD7}; CATALYTIC ACTIVITY: Reaction=ADP(out) + AMP(in) = ADP(in) + AMP(out); Xref=Rhea:RHEA:72851, ChEBI:CHEBI:456215, ChEBI:CHEBI:456216; Evidence={ECO:0000250|UniProtKB:Q86VD7}; CATALYTIC ACTIVITY: Reaction=ADP(out) + dADP(in) = ADP(in) + dADP(out); Xref=Rhea:RHEA:72855, ChEBI:CHEBI:57667, ChEBI:CHEBI:456216; Evidence={ECO:0000250|UniProtKB:Q86VD7}; CATALYTIC ACTIVITY: Reaction=ADP(in) + ATP(out) = ADP(out) + ATP(in); Xref=Rhea:RHEA:34999, ChEBI:CHEBI:30616, ChEBI:CHEBI:456216; Evidence={ECO:0000250|UniProtKB:Q86VD7}; SUBCELLULAR LOCATION: Mitochondrion inner membrane {ECO:0000250|UniProtKB:Q86VD7}; Multi-pass membrane protein {ECO:0000255}. DISRUPTION PHENOTYPE: Morphant embryos show morphological anomalies including dorsal curvature and bent tails, severe muscle disorganization, early motor defects, and mitochondrial abnormalities. {ECO:0000269|PubMed:26541337}. SIMILARITY: Belongs to the mitochondrial carrier (TC 2.A.29) family. {ECO:0000305}. |
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